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Evans-Fisher syndrome: A case report

Abstract:

Introduction: Evans-Fisher syndrome (EFS) is an alteration characterized by the decrease of at least two hematopoietic cell lines in the absence of any other diagnosis. The etiology is unknown, so it is considered an idiopathic disorder, with possible fatal repercussions. Clinical Case: A 19-year-old female patient, who first came to the outpatient clinic of the Hematology Service of the Hospital Homero Castanier Crespo in Azogues city, reporting a heavy metrorrhagia for approximately 4 days. After 3 months of presenting symptoms and ruling out other pathologies, Evans Fisher Syndrome was diagnosed. Evolution: The patient in addition to thrombocytopenia and eosinophilia, presented the signs and symptoms described in the literature for EFS, as time goes by the complications of this pathology such as hyperbilirubinemia, anemia bleeding, even fetal death, and splenic involvement which led to perform a splenectomy, which was the most likely that future pregnancies would have fewer complications. Conclusions: After an extensive investigation of the clinical case, it is possible to reach an uncommon diagnosis in our environment in a joint work of several specialties in the hospital entity and an adequate collaboration of the patient for several years allowed stabilizing her pathology, with a surgical treatment (splenectomy), with the respective follow-up care, presenting even a perfect conditions pregnancy.