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Juvenile systemic sclerosis in an infant: case report

Abstract:

Juvenile systemic scleroderma is a rare chronic pathology of connective tissue, whose symptoms begin on average at age 11. It has a high morbidity and mortality, being a disease of which there is no consensus of treatment, so it becomes a challenge for the specialists who manage it. This paper describes a case of diffuse systemic juvenile cutaneous scleroderma in a one-yearold girl, diagnosed and treated in a multidisciplinary manner at the Baca Ortiz Children s Hospital in Quito, Ecuador, which highlights the importance of maintaining a high level of suspicion, allowing early diagnosis, and carrying out pharmacological and non-pharmacological treatments to stabilize the activity of the disease and improve the quality of life of people affected by this disease.