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Stiff-Man' Syndrome or Stiff-Person' Syndrome. Case presentation

Abstract:

Introduction: the Stiff person's syndrome is a strange and rare neurological reported disease. Objective: a case presentation that contributes in teaching in pre grade and post grade and the general medical community. Case presentation: 60 years old female, presenting painful and frequent muscle spasms in upper body, and both legs, prostration, deformity in her feet of 4 years of evolution. The clinical exam, the Magnetic nuclear Resonance, electromyography and other studies allowed diagnosis. Discussion: therapeutic resources are limited and it is pointed out the discouraging results. The disease progress and causes serious incapacity up to invalidity. Patients have a poor quality of life, serious psychological and economical affections and an excessive index of comorbidity and hospitalizations. Conclusions: it is a rare entity both to clinician and neurologist. Is a disease of a difficult diagnosis. It is the first report in more than 50 years in our institution.